1997; 4 (3):209-23 (ISSN: 1071-9091) Menezes AH. Most of the literature comprises case reports and from varied specialities. 1. After a brief introduction to anatomy, biomedical considerations, and embryology, the multidisciplinary team of authors, led by Professor Goel, discusses in detail the most innovative … craniovertebral junction anomaliesdiagnosis and management PRESENTER- DR ANAND V K MODERATOR- DR P S CHANDRA DEPARTMENT OF NEUROSURGERY AIIMS, NEW DELHI 9/2/2011 RADIOLOGY OF CVJ CRANIOMETRY: Uses a series of lines, planes & angles to define the normal anatomic relationships of the CVJ. Imaging of this complex region and reaching to a specific diagnosis continues to be a challenge for imaging specialists. Craniovertebral Junction Trauma. step-by-step instruction in more than 30 different craniovertebral procedures. Epidemiology Chordomas are rare tumours arising from persistent rests of notochordal remnants. on Craniovertebral Junction Anomalies” submitted by Dr.D.R. 34. A variety of anomalies of bony, meningeal, and neural elements are known to occur in this region, producing a … Found inside – Page 119... Syringomyelia related to abnormalities of the craniovertebral junction. In: Batzdorf U, ed. Syringomyelia: Current Concepts in Diagnosis and Treatment. Cases in Pediatric Acute Care presents over 100 real-world pediatric acute care cases, each including a brief patient history, a detailed history of present illness, presenting signs and symptoms, vital signs, and physical examination ... Objectives: Craniovertebral junction (CVJ) abnormalities constitute a group of treatable neurological disorders, especially in the Indian subcontinent. There is 4.1% risk of vertebral artery injury during craniovertebral junction (CVJ) surgery (2,3). [10, 20, 29] It is correlated with decreased space available at the CVJ which can predispose to myelopathy and traumatic injury. Congenital, developmental, and acquired bony abnormalities result in compression and distortion of the neural structures, the vertebrobasilar vascular system, and the cerebrospinal fluid channels. ... A clivus plate fixation for reconstruction of ventral defect of the craniovertebral junction: Found insideA concise, case-based clinical resource on the topic of imaging in spinal trauma, highly illustrated throughout. Neurosurg Clin N Am. 40). The craniovertebral junction is formed by the occipital condyles, atlas (C1), axis (C2) vertebrae, and their articulations. * Reprint requests: Todd C. Hankinson, MD, Department of Neurosurgery, Columbia University, College of Physicians and Surgeons, 710 West 168th Street, NI Box #132, New York, NY 10032. The craniovertebral junction is the most complex of the axial skeleton, residing between the skull and the upper cervical spine. Organized into four main parts, the book begins by examining the embryology, anatomy, imaging, and biomechanics of the craniovertebral junction, then proceeds to the diagnosis, pathology, and clinical management of disorders affecting this region. Dr. Arnold H. Menezes is a Neurosurgeon in Iowa City, IA. Study Design. Craniovertebral anomalies The CVJ is the site of numerous pathologies, most originating in bone anomalies … This is particularly true in the pediatric population, in which the neurosurgeon is faced with a wide variety of congenital developmental anomalies and acquired diseases and must take into account the need to avoid significant interference ... Congenital Anomalies of the Craniovertebral Junction. The craniovertebral junction is formed by the occipital condyles, atlas (C1), axis (C2) vertebrae, and their articulations. This issue of Acta Neurochirururgica presents the latest surgical and experimental approaches to the craniovertebral junction (CVJ). Found insideThey kindly shared their personal experience and lessons learned over the years. This book is beneficial for all the professionals working in the prenatal diagnosis. Soft Tissue anomalies 1. To evaluate the prevalence of anatomical variations of the vertebral artery at the craniovertebral junction and the posterior arch of the atlas in the US population.. Summary of Background Data. AbstractOBJECTIVE AND IMPORTANCE:. Found inside – Page 2222Diagnostic neurological investigations , such as brain Goel , A. et al . ... “ Craniovertebral junction anomalies : Diagnosis and treatment , ” Semin ... Management of proatlas segmentation anomalies is aimed at (1) relieving the neural compression, if any and (2) stabilizing the craniovertebral junction, if there is instability of this region. CHARGE syndrome is a widespread malformation that was originally described independently by Hall 1 and Hittner et al. Introduction. Prescher A. Affected individuals often undergo head and neck imaging to assess abnormalities of the olfactory structures, hypothalamus-pituitary axis, and inner ear. I Foundations for Surgical Treatment. Ann Otol Rhinol Laryngol. Shankar DR. A comprehensive study on craniovertebral junction anomalies. Congenital, developmental, and acquired bony abnormalities result in compression and distortion of the neural structures, the vertebrobasilar vascular system, and the cerebrospinal fluid channels. Found inside – Page iThese are followed by detailed sections covering all aspects of neuroanesthesia and neurointensive care in both adult and pediatric patients. The final chapter discusses ethical and legal issues. This multidisciplinary work - the first since 1977 devoted specifically to craniovertebral surgery -includes contributions from the most respected authorities in the field, and offers neurosurgeons practical, step-by-step instruction in ... Embryology, classification and surgical management of bony malformations of the craniovertebral junction. Anomalies of the Craniovertebral Junction; Anomalies of the Occiput; Anomalies of the Atlas; Posterior Arch Anomalies; Anomalies of the Axis; Acquired Conditions Affecting the Craniovertebral Junction; Other Conditions; References; III Atlantoaxial Dislocation. Found inside – Page 80Treatment • Conservative approach initially unless unstable or neural deficits o Traction , cervical orthosis , activity restriction Symptomatic , refractory to ... Menezes AH : Craniovertebral junction anomalies : diagnosis and management . In C. Di Rocco, & N. Akalan Eds., 2013. Found inside – Page 1828Craniovertebral junction anomalies: Diagnosis and management. Seminars in Pediatric Neurology, 4, 209–223. Menezes, A. H. (2008). Abstract. Basilar invagination forms a prominent component of the craniovertebral anomalies. Four patients with craniovertebral junction anomalies (CVJ) and Klippel-Feil cervical fusion defects associated with dermoid Found insideAnatomy and biomechanics of normal craniovertebral junction (a) and biomechanics of stabilization (b). Childs Nerv ... A rational approach to surgical treatment in children. ... Craniovertebral junction anomalies: diagnosis and management. Craniovertebral junction (CVJ) disorders in the Occident are usually associated with systemic disorders. In contrast, in the Orient, a greater incidence of isolated CVJ anomalies is seen. Although these are developmental anomalies, they manifest late in life, with trauma and/or infection playing a promotive role. Craniovertebral junction abnormalities can be developmental, genetic, or acquired in origin. Symptomatic anomalies of the craniovertebral junction (CVJ) present a unique challenge for neurosurgical management with regard to surgical approach selection and planning and the accompanying technical difficulty. Found inside – Page iiThese are followed by sections on differential diagnosis, treatment and prognosis. Finally, the book closes with an extensive discussion on research, related pathologies and patient resources. Godlewski S. Quelques apports récents sur les anomalies congénitales de la charnière cervico-occipitale. The junction between the head and neck is called the occipitocervical or craniovertebral junction (CVJ). case report History and Examination The patient was a 7-year-old boy who initially pre-sented to the pediatric neurology service for evaluation of seizure-like episodes, as described by his parents, for the preceding 6 months. 1 Embryology, Development, and Classification of Disorders of the Craniovertebral Junction. 34. Although modern imaging technologies usually permit an accurate diagnosis at an early stage, syringomyelia remains an enigmatic condition. Fig. Fig. Craniovertebral Junction Anomalies: Diagnosis and Management Arnold H. Menezes The craniovertebral junction is the most complex of the axial skeleton, residing between the skull and the upper cervical spine. Vertebral artery anomalies The failure of completion of ossification of the craniovertebral junction and especially the atlantal arch and odontoid process An interesting finding in our patients was the extremely until the age of 9 years makes the diagnosis of AAD difficult high incidence of variations in the VA anatomy especially to establish [22]. Surgery is often indicated to prevent or treat neurological symptoms. Found inside – Page 22Menezes AH: Nosographic identification and management of pediatric craniovertebral junction anomalies: evolution of concepts and modalities of treatment. The bones of the neck that are affected are cervical vertebrae (C1 - C7). For this purpose a systematic review of the literature … Greater awareness of this subset of patients is essential for greater understanding and effective management of these ailments. Craniovertebral Junction Abnormalities in Down Syndrome. Once the stage is set by congenital craniovertebral anomalies, the developmental and acquired phenomena may supervene and produce atlantoaxial instability and subsequently basilar invagination. Distinguished physicians and researchers from prestigious Cancer Centers around the world offer their expertise in current and innovative management of cancer in the spine. The neural arch ossification centers form during the seventh gestational week, whereas the ossification center within the body of C1 becomes visible during the first year of life. Introduction Fig. Found insideThis book covers the complete gamut of neuroradiology cases, including normal anatomy, pitfalls, and artifacts across the brain and spine in a single volume, enriched with high-resolution images that support the interpretation of CT and MRI ... This series, sponsored by the European Association of Neurosurgical Societies, has already become a classic. 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